Oral manifestations of Ehlers-Danlos syndrome.

نویسندگان

  • Y Létourneau
  • R Pérusse
  • H Buithieu
چکیده

Ehlers-Danlos syndrome is a rare hereditary disease of the connective tissue which can present oral manifestations. A brief history of the disease is presented along with the epidemiology and characteristics of the 8 main phenotypes of the syndrome. The article also describes the case of a 12-year-old patient presenting with hypermobility of the temporo-mandibular joint and capillary fragility, and highlights the precautions to take when treating patients with this syndrome.

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عنوان ژورنال:
  • Journal

دوره 67 6  شماره 

صفحات  -

تاریخ انتشار 1989